A case of large leiomyoma arising from rudimentary horn in Mayer Rokitansky-Küster-Hauser syndrome, managed by minimally invasive surgery

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a congenital disorder marked by aplasia or hypoplasia of the uterus and vagina as result arrest in development müllerian ducts. Prevalence being 1 4000–5000 live births females. Leiomyoma most common uterine tumor, their occurrence from rudimentary females with MRKH very rare only few cases have been documented literature. Here we report 38-year-old female, known case presenting USG suggestive 7.9x7.4x6.0 leiomyoma proximity to hypoplastic uterus, undergoing laparoscopic removal fibroid right ovarian cystectomy (incidental finding). Therefore, it important consider such unusual diagnosis fibroids originating primitive horns while treating these patients for gynecological symptoms well infertility, them managing endoscopically.